What is the definition of Long QT Syndrome 1?

Romano-Ward syndrome is the most common form of inherited long QT syndrome. Symptoms include arrhythmia, fainting, cardiac arrest, and sudden death. There are six different types of this syndrome, long QT 1 through 6. Each type is caused by a change in a different gene. The most prevalent form of long QT syndrome is long QT type 1. Long QT type 1 is caused by changes in the KCNQ1 gene. Romano-Ward syndrome is inherited in an autosomal dominant fashion.

What are the alternative names for Long QT Syndrome 1?

  • LQT1
  • Romano-Ward syndrome
  • Ward-Romano syndrome
  • Ventricular fibrillation with prolonged QT interval
  • Condition: Long QT Syndrome
  • Journal: JACC. Clinical electrophysiology
  • Treatment Used: Left Cardiac Sympathetic Denervation
  • Number of Patients: 185
  • Published —
The study researched the effect of left cardiac sympathetic denervation (removal of some of the spinal cord) for long QT syndrome.
  • Condition: Inherited Cardiac Arrhythmia Syndrome in Children
  • Journal: Zhonghua er ke za zhi = Chinese journal of pediatrics
  • Treatment Used: Implantable Cardioverter Defibrillator (ICD) Implantation
  • Number of Patients: 30
  • Published —
This study analyzed and summarized the diagnosis and treatment experience of common inherited cardiac arrhythmia (heart quivering) syndrome in pediatric patients, and explored the most appropriate therapy.