Phase 3 Study of the Efficacy and Safety of ION582 in Children and Adults With Angelman Syndrome

Status: Recruiting
Location: See all (6) locations...
Intervention Type: Drug
Study Type: Interventional
Study Phase: Phase 3
SUMMARY

The purpose of this study is to evaluate the efficacy and safety of ION582 in children and adults with Angelman syndrome caused by a deletion or mutation of the UBE3A gene.

Eligibility
Participation Requirements
Sex: All
Minimum Age: 2
Maximum Age: 50
Healthy Volunteers: f
View:

• The participants caregiver(s)/ legally authorized representative must have given written informed consent and any authorizations required by local law and be able to comply with all study requirements.

• Medically stable and can undergo sedation and/or general anesthesia without intubation.

• Male or female between 2 and lesser than or equal to (≤)50 years of age, depending on specific cohort, at the time of the in-clinic Screening visit.

• Participant has a documented diagnosis of Angelman syndrome (AS) due to either Ubiquitin-protein ligase E3A (UBE3A) deletion or UBE3A mutation.

• Currently receiving stable doses of concomitant medications typically prescribed for AS, such as anti-epileptic medication, behavioral management medications, sleep medications, gabapentin, cannabidiol, and special diets, supplements, or nutritional support for at least 8 weeks prior to the Baseline visit.

• Legally authorized representative/caregiver(s) agree(s) not to post any of the participant's personal medical data or information related to the study on any website or social media site (e.g., Facebook, Instagram, Twitter, YouTube, TikTok, etc.) from the time of enrollment until they are notified that the study is completed.

Locations
United States
California
Rady Children's Hospital
RECRUITING
San Diego
Colorado
Colorado Children's Hospital Research Institute
RECRUITING
Aurora
Florida
Nicklaus Children's Hospital
RECRUITING
Miami
Illinois
Rush University Medical Center
RECRUITING
Chicago
Missouri
Children's Mercy
RECRUITING
Kansas City
North Carolina
University of North Carolina at Chapel Hill School of Medicine
RECRUITING
Carrboro
Contact Information
Primary
Ionis Pharmaceuticals, Inc.
IonisION582-CS2@clinicaltrialmedia.com
(844) 285-7172
Time Frame
Start Date: 2025-06-10
Estimated Completion Date: 2030-04
Participants
Target number of participants: 210
Treatments
Experimental: Cohort 1 ION582 40 milligrams (mg)
Participants (aged 2 to \<18 years old) will be administered ION582 40 mg via intrathecal (IT) injection every 12 weeks (Q12W) during the double blind and LTE treatment periods.
Experimental: Cohort 1 ION582 80 mg
Participants (aged 2 to \<18 years old) will be administered ION582 80 mg via IT injection Q12W during the double blind and LTE treatment periods.
Placebo_comparator: Cohort 1 Placebo
Participants (aged 2 to \<18 years old) will be administered ION582 matching placebo via IT injection Q12W during the double-blind treatment period and then administered ION582 40 mg or 80 mg Q12W during the LTE treatment period.
Experimental: Cohort 2 ION582 40 mg
Participants (aged 18 to ≤50 years old) will be administered ION582 40 mg via IT injection Q12W during the double blind and LTE treatment periods.
Experimental: Cohort 2 ION582 80 mg
Participants (aged 18 to ≤50 years old) will be administered ION582 80 mg via IT injection Q12W during the double blind and LTE treatment periods.
Placebo_comparator: Cohort 2 Placebo
Participants (aged 18 to ≤50 years old) will be administered ION582 matching placebo via IT injection Q12W during the double-blind treatment period and then randomized to ION582 40 mg or 80 mg Q12W during the LTE treatment period.
Related Therapeutic Areas
Sponsors
Leads: Ionis Pharmaceuticals, Inc.

This content was sourced from clinicaltrials.gov