NBIAready: Online Collection of Natural History Patient-reported Outcome Measures

Status: Unknown
Location: See location...
Study Type: Observational
SUMMARY

The purpose of this study is to learn more about Neurodegeneration with Brain Iron Accumulation (NBIA) Disorders. Data is being collected on three types of NBIA disorders: Pantothenate Kinase-Associated Neurodegeneration (PKAN), PLA2G6-associated Neurodegeneration (PLAN) and Beta-propeller Protein-associated Neurodegeneration (BPAN). The study will (1) collect information about how symptoms and findings in NBIA change over time and (2) identify measures of NBIA that can be used in future clinical trials. Participants will follow links to a secure website every 6 months for a period of 5-10 years to electronically complete a set of rating scales as related to their NBIA disorder.

Eligibility
Participation Requirements
Sex: All
Healthy Volunteers: f
View:

• Diagnosis of PKAN, PLAN or BPAN confirmed by gene testing and/or clinical features.

• Ability to access a computer with internet services or a phone approximately once every 6 months for up to 10 years to enter data.

Locations
United States
Oregon
Oregon Health & Science University
RECRUITING
Portland
Contact Information
Primary
Alison C Freed, BA
freeal@ohsu.edu
503 494 6838
Backup
Allison M Gregory, MS, CGC
gregorya@ohsu.edu
503 494 4344
Time Frame
Start Date: 2015-04
Completion Date: 2025-04
Participants
Target number of participants: 300
Treatments
PKAN
This group consists of individuals diagnosed with PKAN using a combination of MRI, other clinical findings, and PANK2 gene sequencing.
PLAN
This group consists of individuals diagnosed with PLAN using a combination of MRI, other clinical findings and PLA2G6 gene sequencing.
BPAN
This group consists of individuals diagnosed with BPAN using a combinatino of MRI, other clinical findings, and WDR45 gene sequencing.
Sponsors
Collaborators: Oregon Health and Science University
Leads: Susan J. Hayflick

This content was sourced from clinicaltrials.gov