Isabelle Fajac

Paris, France

Last Updated: 09/26/2026

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Found 64 publications

Persistence of static lung hyperinflation in adults with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor.

Persistence of static lung hyperinflation in adults with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor.

Journal: Thorax

Published: March 30, 2026

Therapeutic revolution for cystic fibrosis

Therapeutic revolution for cystic fibrosis

Journal: La Revue du praticien

Published: January 23, 2026

Ageing with cystic fibrosis: Challenges ahead.

Ageing with cystic fibrosis: Challenges ahead.

Journal: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society

Published: October 09, 2025

Safety and efficacy of elexacaftor/tezacaftor/ivacaftor in adolescents and adults with cystic fibrosis and F508del-gating and F508del-residual function genotypes: results from an open-label extension study.

Safety and efficacy of elexacaftor/tezacaftor/ivacaftor in adolescents and adults with cystic fibrosis and F508del-gating and F508del-residual function genotypes: results from an open-label extension study.

Journal: Annals of the American Thoracic Society

Published: October 03, 2025

The role of sweat chloride in determining CFTR protein restoration in people with cystic fibrosis.

The role of sweat chloride in determining CFTR protein restoration in people with cystic fibrosis.

Journal: The Lancet. Respiratory medicine

Published: August 29, 2025

Elexacaftor/tezacaftor/ivacaftor for cystic fibrosis and rare CFTR variants: in vitro translation to a phase 3, double-blind, randomized, placebo-controlled trial, and real-world study.

Elexacaftor/tezacaftor/ivacaftor for cystic fibrosis and rare CFTR variants: in vitro translation to a phase 3, double-blind, randomized, placebo-controlled trial, and real-world study.

Journal: American journal of respiratory and critical care medicine

Published: June 13, 2025

The clinical, psychosocial, and economic burden of cystic fibrosis lung disease in the era of CFTR modulator therapy.

The clinical, psychosocial, and economic burden of cystic fibrosis lung disease in the era of CFTR modulator therapy.

Journal: Annals of the American Thoracic Society

Published: March 14, 2025

Cystic Fibrosis Microbiome-directed Antibiotic Therapy Trial in Exacerbations Results Stratified (CFMATTERS): results of a multicentre randomised controlled trial.

Cystic Fibrosis Microbiome-directed Antibiotic Therapy Trial in Exacerbations Results Stratified (CFMATTERS): results of a multicentre randomised controlled trial.

Journal: The European respiratory journal

Published: December 12, 2024

Sweat chloride reflects CFTR function and correlates with clinical outcomes following CFTR modulator treatment.

Sweat chloride reflects CFTR function and correlates with clinical outcomes following CFTR modulator treatment.

Journal: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society

Published: August 11, 2024

Efficacy and safety of CFTR modulators in patients with interstitial lung disease caused by ABCA3 transporter deficiency.

Efficacy and safety of CFTR modulators in patients with interstitial lung disease caused by ABCA3 transporter deficiency.

Journal: ERJ open research

Published: July 12, 2024

New drugs, new challenges in cystic fibrosis care.

New drugs, new challenges in cystic fibrosis care.

Journal: European respiratory review : an official journal of the European Respiratory Society

Published: March 05, 2024

ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals.

ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals.

Journal: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society

Published: November 20, 2023

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Last Updated: 09/26/2026