Maria B. Bagh
244, A J C Bose Road
Kolkata, WB, India
Kolkata, WB, India
Last Updated: 09/26/2026
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Found 13 publications
Niemann Pick C1 mistargeting disrupts lysosomal cholesterol homeostasis contributing to neurodegeneration in a Batten disease model.
Journal: Science advances
Published: May 07, 2025
Disruption of lysosomal nutrient sensing scaffold contributes to pathogenesis of a fatal neurodegenerative lysosomal storage disease.
Journal: The Journal of biological chemistry
Published: June 06, 2023
Ppt1-deficiency dysregulates lysosomal Ca++ homeostasis contributing to pathogenesis in a mouse model of CLN1 disease.
Journal: Journal of inherited metabolic disease
Published: October 08, 2021
Ablation of microRNA-155 and neuroinflammation in a mouse model of CLN1-disease.
Journal: Biochemical and biophysical research communications
Published: May 24, 2021
In a mouse model of INCL reduced S-palmitoylation of cytosolic thioesterase APT1 contributes to microglia proliferation and neuroinflammation.
Journal: Journal of inherited metabolic disease
Published: December 10, 2020
Cln1-mutations suppress Rab7-RILP interaction and impair autophagy contributing to neuropathology in a mouse model of infantile neuronal ceroid lipofuscinosis.
Journal: Journal of inherited metabolic disease
Published: November 15, 2019
Cln3-mutations underlying juvenile neuronal ceroid lipofuscinosis cause significantly reduced levels of Palmitoyl-protein thioesterases-1 (Ppt1)-protein and Ppt1-enzyme activity in the lysosome.
Journal: Journal of inherited metabolic disease
Published: November 28, 2018
Emerging new roles of the lysosome and neuronal ceroid lipofuscinoses.
Journal: Molecular neurodegeneration
Published: July 12, 2018
Misrouting of v-ATPase subunit V0a1 dysregulates lysosomal acidification in a neurodegenerative lysosomal storage disease model.
Journal: Nature communications
Published: April 26, 2016
Suppression of agrin-22 production and synaptic dysfunction in Cln1 (-/-) mice.
Journal: Annals of clinical and translational neurology
Published: August 03, 2015
Cln1 gene disruption in mice reveals a common pathogenic link between two of the most lethal childhood neurodegenerative lysosomal storage disorders.
Journal: Human molecular genetics
Published: April 09, 2015
Combination of N-acetylcysteine, α-lipoic acid and α-tocopherol substantially prevents the brain synaptosomal alterations and memory and learning deficits of aged rats.
Journal: Experimental gerontology
Published: September 21, 2013
Last Updated: 09/26/2026