Paula Clemente
Stockholm, AB 17165, Sweden
Last Updated: 09/26/2026
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Found 10 publications
ANGEL2 phosphatase activity is required for non-canonical mitochondrial RNA processing.
Journal: Nature communications
Published: March 15, 2022
The one-carbon pool controls mitochondrial energy metabolism via complex I and iron-sulfur clusters.
The one-carbon pool controls mitochondrial energy metabolism via complex I and iron-sulfur clusters.
Journal: Science advances
Published: October 01, 2020
Defects of mitochondrial RNA turnover lead to the accumulation of double-stranded RNA in vivo.
Journal: PLoS genetics
Published: February 25, 2019
Mutations in the mitochondrial tryptophanyl-tRNA synthetase cause growth retardation and progressive leukoencephalopathy.
Journal: Molecular genetics & genomic medicine
Published: November 13, 2018
SQSTM1/p62-Directed Metabolic Reprogramming Is Essential for Normal Neurodifferentiation.
Journal: Stem cell reports
Published: January 25, 2018
Myoglobinopathy is an adult-onset autosomal dominant myopathy with characteristic sarcoplasmic inclusions.
Journal: Nature communications
Published: September 14, 2017
A multi-systemic mitochondrial disorder due to a dominant p.Y955H disease variant in DNA polymerase gamma.
Journal: Human molecular genetics
Published: February 24, 2017
Mitochondrial Polyadenylation Is a One-Step Process Required for mRNA Integrity and tRNA Maturation.
Mitochondrial Polyadenylation Is a One-Step Process Required for mRNA Integrity and tRNA Maturation.
Journal: PLoS genetics
Published: February 12, 2016
SUV3 helicase is required for correct processing of mitochondrial transcripts.
Journal: Nucleic acids research
Published: March 11, 2015
Showing 1-10 of 10
Last Updated: 09/26/2026