Stuart L. Johnson

Sheffield, ENG, United Kingdom

Last Updated: 09/26/2026

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Found 52 publications

HDAC6 inhibition alleviates mitochondrial trafficking in novel models of Charcot-Marie-Tooth Disease Type 2A.

HDAC6 inhibition alleviates mitochondrial trafficking in novel models of Charcot-Marie-Tooth Disease Type 2A.

Journal: JCI insight
Published: July 14, 2026

Aging Alters Hair Cell Physiological Properties in Mice With Late-Onset Age-Related Hearing Loss.

Aging Alters Hair Cell Physiological Properties in Mice With Late-Onset Age-Related Hearing Loss.

Journal: Aging cell
Published: November 21, 2025

Mechanisms driving the functional maturation of the developing mammalian auditory pathway.

Mechanisms driving the functional maturation of the developing mammalian auditory pathway.

Journal: Current topics in developmental biology
Published: September 19, 2025

Myosin 7a is required for maintaining the transducing stereocilia and for force transmission to the MET channel during cochlear hair cell development.

Myosin 7a is required for maintaining the transducing stereocilia and for force transmission to the MET channel during cochlear hair cell development.

Journal: The Journal of physiology
Published: June 27, 2025

Adeno-associated virus-based rescue of Myo7a expression restores hair-cell function and improves hearing thresholds in a USH1B mouse strain.

Adeno-associated virus-based rescue of Myo7a expression restores hair-cell function and improves hearing thresholds in a USH1B mouse strain.

Journal: The Journal of physiology
Published: June 18, 2025

Transient capacitance changes recorded from vestibular type I hair cells are produced by GK,L gating and do not involve neurotransmitter exocytosis.

Transient capacitance changes recorded from vestibular type I hair cells are produced by GK,L gating and do not involve neurotransmitter exocytosis.

Journal: The Journal of physiology
Published: February 11, 2025

MYO7A is required for the functional integrity of the mechanoelectrical transduction complex in hair cells of the adult cochlea.

MYO7A is required for the functional integrity of the mechanoelectrical transduction complex in hair cells of the adult cochlea.

Journal: Proceedings of the National Academy of Sciences of the United States of America
Published: January 02, 2025

In vivo AAV9-Myo7a gene rescue restores hearing and cholinergic efferent innervation in inner hair cells.

In vivo AAV9-Myo7a gene rescue restores hearing and cholinergic efferent innervation in inner hair cells.

Journal: JCI insight
Published: April 16, 2024

Pleiotropic brain function of whirlin identified by a novel mutation.

Pleiotropic brain function of whirlin identified by a novel mutation.

Journal: iScience
Published: March 11, 2024

The upregulation of K+ and HCN channels in developing spiral ganglion neurons is mediated by cochlear inner hair cells.

The upregulation of K+ and HCN channels in developing spiral ganglion neurons is mediated by cochlear inner hair cells.

Journal: The Journal of physiology
Published: December 14, 2023

BAI1 localizes AMPA receptors at the cochlear afferent post-synaptic density and is essential for hearing.

BAI1 localizes AMPA receptors at the cochlear afferent post-synaptic density and is essential for hearing.

Journal: Cell reports
Published: September 14, 2023

A critical period of prehearing spontaneous Ca2+ spiking is required for hair-bundle maintenance in inner hair cells.

A critical period of prehearing spontaneous Ca2+ spiking is required for hair-bundle maintenance in inner hair cells.

Journal: The EMBO journal
Published: July 16, 2022
Showing 1-12 of 52

Last Updated: 09/26/2026