Congenital coronary artery malformation, also known as coronary artery anomaly (CAA), is a condition in which a coronary artery has an abnormality that is present at birth. The function of the coronary arteries is to supply oxygen to the heart muscle.

Congenital coronary artery malformation may not have any symptoms, or symptoms may not appear until late adolescence or adulthood. Symptoms in infants and children may include poor feeding, sweating, pale skin, and difficulty breathing. Symptoms in teens and adults may include fatigue, shortness of breath when at rest or upon exertion, dizziness and fainting during exercise, fluid retention, and chest pain. Other, more serious symptoms of congenital coronary artery malformation may include heart failure or sudden cardiac death.

Treatment for congenital coronary artery malformations depends on the severity and type of anomaly. Treatment may include avoiding excessive exercise; medications, such as diuretics, beta blockers, and antiarrhythmics; oxygen therapy; percutaneous coronary interventions; or surgery.