Congenital Pulmonary Lymphangiectasia
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Congenital Pulmonary Lymphangiectasia Overview

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Learn About Congenital Pulmonary Lymphangiectasia

What is the definition of Congenital Pulmonary Lymphangiectasia?
Congenital pulmonary lymphangiectasia (CPL) is a rare developmental disorder that affects the lungs. It is present from birth and usually becomes apparent in the first few days of life with respiratory failure. It sometimes is apparent before birth with non-immune hydrops fetalis and pleural effusion (fluid in the lung). Infants with CPL often develop severe, potentially life-threatening, respiratory distress shortly after birth. They may also develop cyanosis caused by low oxygen levels in the blood, which causes the skin to have a bluish tint. Symptoms are due to abnormally wide (dilated) lymphatic vessels within the lungs. These vessels drain a fluid called lymph from different areas of the body. They are an important part of the lymphatic system, which helps the immune system protect the body against infection and disease. The underlying cause of CPL is unknown. It can occur as a primary or secondary disorder (due to another underlying condition). Primary CPL occurs as an isolated defect or as part of a generalized form of lymphatic disease affecting the whole body. Secondary CPL can occur due to a variety of heart abnormalities or lymphatic obstruction. Some cases of CPL have been associated with genetic disorders.
What are the alternative names for Congenital Pulmonary Lymphangiectasia?
  • Congenital pulmonary lymphangiectasia
  • CPL
  • Lymphangiectasia pulmonary congenital
  • Lymphangiomatosis pulmonary
  • Pulmonary cystic lymphangiectasis
Who are the top Congenital Pulmonary Lymphangiectasia Local Doctors?
Elite in Congenital Pulmonary Lymphangiectasia
Dr. Maxim G. Itkin
Pediatric Radiology | Interventional Radiology
Elite in Congenital Pulmonary Lymphangiectasia
Dr. Maxim G. Itkin
Pediatric Radiology | Interventional Radiology
Referral may be required

Penn Interventional Radiology Perelman

3400 Civic Center Boulevard, Atrium, Ground Floor, 
Philadelphia, PA 
Languages Spoken:
English, Hebrew, Russian
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Accepting New Patients
Offers Telehealth

Maxim Itkin is a Pediatric Radiologist and an Interventional Radiologist practicing medicine in Philadelphia, Pennsylvania. Dr. Itkin is rated as an Elite provider by MediFind in the treatment of Congenital Pulmonary Lymphangiectasia. He is also highly rated in 7 other conditions, according to our data. His clinical expertise encompasses Chylous Ascites, Congenital Pulmonary Lymphangiectasia, Ascites, Gastrostomy, and Angioplasty. Dr. Itkin is board certified in American Board Of Radiology and Radiology/IR And Diag (AMA). Dr. Itkin is currently accepting new patients.

Distinguished in Congenital Pulmonary Lymphangiectasia
Dr. Francis X. Mccormack
Pulmonary Medicine
Distinguished in Congenital Pulmonary Lymphangiectasia
Dr. Francis X. Mccormack
Pulmonary Medicine
Referral may be required

Office

200 Eden Ave, 
Cincinnati, OH 
513-475-8523
Languages Spoken:
English
See accepted insurances
Accepting New Patients

Francis Mccormack is a Pulmonary Medicine provider practicing medicine in Cincinnati, Ohio. Dr. Mccormack is rated as a Distinguished provider by MediFind in the treatment of Congenital Pulmonary Lymphangiectasia. He is also highly rated in 11 other conditions, according to our data. His clinical expertise encompasses Lymphangioleiomyomatosis, Congenital Pulmonary Lymphangiectasia, Pulmonary Fibrosis, Interstitial Lung Disease, and Lung Transplant. Dr. Mccormack is currently accepting new patients.

 
 
 
 
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Experienced in Congenital Pulmonary Lymphangiectasia
Dr. Vatsala Ramprasad
Pediatric Pulmonology | Sleep Medicine
Experienced in Congenital Pulmonary Lymphangiectasia
Dr. Vatsala Ramprasad
Pediatric Pulmonology | Sleep Medicine
Referral may be required

St. Christopher's Pediatric Associates Pulmonary & Allergy - E. Erie Avenue

160 E Erie Ave, 
Philadelphia, PA 
215-427-5183
Languages Spoken:
English
See accepted insurances
Accepting New Patients

Vatsala Ramprasad is a Pediatric Pulmonologist and a Sleep Medicine provider practicing medicine in Philadelphia, Pennsylvania. Dr. Ramprasad is rated as an Experienced provider by MediFind in the treatment of Congenital Pulmonary Lymphangiectasia. She is also highly rated in 1 other condition, according to our data. Her clinical expertise encompasses Asthma, Obstructive Sleep Apnea, Congenital Pulmonary Lymphangiectasia, and Congenital Central Hypoventilation Syndrome. Dr. Ramprasad is board certified in American Board Of Pediatrics. Dr. Ramprasad is currently accepting new patients.

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Published Date: May 02, 2022
Published By: Genetic and Rare Diseases Informnation Center