Congenital Pulmonary Lymphangiectasia
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Congenital Pulmonary Lymphangiectasia Overview

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Learn About Congenital Pulmonary Lymphangiectasia

What is the definition of Congenital Pulmonary Lymphangiectasia?
Congenital pulmonary lymphangiectasia (CPL) is a rare developmental disorder that affects the lungs. It is present from birth and usually becomes apparent in the first few days of life with respiratory failure. It sometimes is apparent before birth with non-immune hydrops fetalis and pleural effusion (fluid in the lung). Infants with CPL often develop severe, potentially life-threatening, respiratory distress shortly after birth. They may also develop cyanosis caused by low oxygen levels in the blood, which causes the skin to have a bluish tint. Symptoms are due to abnormally wide (dilated) lymphatic vessels within the lungs. These vessels drain a fluid called lymph from different areas of the body. They are an important part of the lymphatic system, which helps the immune system protect the body against infection and disease. The underlying cause of CPL is unknown. It can occur as a primary or secondary disorder (due to another underlying condition). Primary CPL occurs as an isolated defect or as part of a generalized form of lymphatic disease affecting the whole body. Secondary CPL can occur due to a variety of heart abnormalities or lymphatic obstruction. Some cases of CPL have been associated with genetic disorders.
What are the alternative names for Congenital Pulmonary Lymphangiectasia?
  • Congenital pulmonary lymphangiectasia
  • CPL
  • Lymphangiectasia pulmonary congenital
  • Lymphangiomatosis pulmonary
  • Pulmonary cystic lymphangiectasis
Who are the top Congenital Pulmonary Lymphangiectasia Local Doctors?
Elite in Congenital Pulmonary Lymphangiectasia
Dr. Maxim Itkin
Pediatric Radiology | Radiology | Interventional Radiology
Elite in Congenital Pulmonary Lymphangiectasia
Dr. Maxim Itkin
Pediatric Radiology | Radiology | Interventional Radiology

Nemours Children's Hospital, Delaware

1600 Rockland Road, 
Wilmington, DE 
800-416-4441
Languages Spoken:
English, Hebrew, Russian
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Maxim Itkin is a Pediatric Radiologist and a Radiologist practicing medicine in Wilmington, Delaware. Dr. Itkin is rated as an Elite provider by MediFind in the treatment of Congenital Pulmonary Lymphangiectasia. He is also highly rated in 10 other conditions, according to our data. His clinical expertise encompasses Chylous Ascites, Congenital Pulmonary Lymphangiectasia, Ascites, Gastrostomy, and Angioplasty. Dr. Itkin is board certified in American Board Of Radiology.

Distinguished in Congenital Pulmonary Lymphangiectasia
Dr. Teresa Victoria
Pediatric Radiology
Distinguished in Congenital Pulmonary Lymphangiectasia
Dr. Teresa Victoria
Pediatric Radiology

Massachusetts General Hospital

55 Fruit St, 
Boston, MA 
617-724-4207
Languages Spoken:
English

Teresa Victoria is a Pediatric Radiologist practicing medicine in Boston, Massachusetts. Dr. Victoria is rated as a Distinguished provider by MediFind in the treatment of Congenital Pulmonary Lymphangiectasia. She is also highly rated in 3 other conditions, according to our data. Her clinical expertise encompasses Congenital Pulmonary Lymphangiectasia, Omphalocele, Diaphragmatic Hernia, and Aicardi-Goutieres Syndrome.

 
 
 
 
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Distinguished in Congenital Pulmonary Lymphangiectasia
Dr. Jack Rychik
Pediatric Cardiology
Distinguished in Congenital Pulmonary Lymphangiectasia
Dr. Jack Rychik
Pediatric Cardiology

Children's Hospital Of Philadelphia

3401 Civic Center Blvd, 
Philadelphia, PA 
215-590-1000
Languages Spoken:
English
See accepted insurances

Jack Rychik is a Pediatric Cardiologist practicing medicine in Philadelphia, Pennsylvania. Dr. Rychik is rated as a Distinguished provider by MediFind in the treatment of Congenital Pulmonary Lymphangiectasia. He is also highly rated in 16 other conditions, according to our data. His clinical expertise encompasses Hypoplastic Left Heart Syndrome (HLHS), Congenital Heart Disease (CHD), Lymphangiectasis, Congenital Pulmonary Lymphangiectasia, and Heart Transplant.

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Published Date: May 02, 2022
Published By: Genetic and Rare Diseases Informnation Center