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Learn About Desmoplastic Small Round Cell Tumor

What is the definition of Desmoplastic Small Round Cell Tumor?
Desmoplastic small round cell tumor (DSRCT) is a rare type of soft tissue cancer (sarcoma) that usually begins in the abdomen. It primarily affects children and young adults and is more common in males. It is formed by small, round cancer cells surrounded by scar-like tissue and is often found in the tissue (peritoneum) that lines the inside of the abdomen and pelvis. The tumor cells have a characteristic genetic change involving a translocation between chromosomes 11 and 22, which is important in differentiating from other similar tumors. The genetic change involved in DSRCT is acquired throughout a person's lifetime and is not inherited. Symptoms may include abdominal pain and a feeling of fullness, abdominal mass, and symptoms of gastrointestinal obstruction, such as constipation.
What are the alternative names for Desmoplastic Small Round Cell Tumor?
  • Desmoplastic small round cell tumor
  • DSRCT
  • Desmoplastic small round-cell tumor
Who are the top Desmoplastic Small Round Cell Tumor Local Doctors?
Mark A. Dickson
Elite in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Hematology | Oncology
Elite in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Hematology | Oncology

Memorial Solid Tumor Group

160 E 53rd St, 
New York, NY 
Languages Spoken:
English
Offers Telehealth

Mark Dickson is a Hematologist Oncology specialist and a Hematologist in New York, New York. Dr. Dickson is rated as an Elite provider by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. His top areas of expertise are Adult Soft Tissue Sarcoma, Liposarcoma, Undifferentiated Pleomorphic Sarcoma, Gastrointestinal Stromal Tumor, and Endoscopy.

Elite in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Hematology | Oncology
Elite in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Hematology | Oncology

Memorial Solid Tumor Group

160 E 53rd St, 
New York, NY 
Languages Spoken:
English
Offers Telehealth

William Tap is a Hematologist Oncology specialist and a Hematologist in New York, New York. Dr. Tap is rated as an Elite provider by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. His top areas of expertise are Adult Soft Tissue Sarcoma, Gastrointestinal Stromal Tumor, Angiosarcoma, Tissue Biopsy, and Liver Embolization.

 
 
 
 
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Andrea L. Ferrari
Elite in Desmoplastic Small Round Cell Tumor
Elite in Desmoplastic Small Round Cell Tumor
Milan, IT 

Andrea Ferrari practices in Milan, Italy. Ms. Ferrari is rated as an Elite expert by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. Her top areas of expertise are Rhabdomyosarcoma, Adult Soft Tissue Sarcoma, Desmoplastic Small Round Cell Tumor, Thyroidectomy, and Pancreatectomy.

What are the latest Desmoplastic Small Round Cell Tumor Clinical Trials?
Allogeneic Stem Cell Transplantation Utilizing Alpha/Beta T Cell and CD19+ B Cell Depletion With Zoledronic Acid in Combination to Treat Pediatric, Adolescent, and Young Adult Patients With Relapsed/Refractory Solid Tumors

Summary: Hematopoietic stem cell transplantation can cure patients with blood cancer and other underlying diseases. αβ-T cell and B cell depletion has been introduced to decrease GVHD and PTLD and has demonstrated effectiveness for hematologic malignancies and non-malignant diseases additionally increasing the donor pool as to allow for haploidentical transplant to safely occur. While solid tumors can be h...

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Lurbinectedin in FET-Fusion Tumors (LIFFT)

Summary: The purpose of this study is to find out if a drug called lurbinectedin (the study drug) is safe and effective at treating people with recurrent or relapsed solid tumors, including Ewing sarcoma.

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Published Date: May 02, 2022
Published By: Genetic and Rare Diseases Informnation Center