Desmoplastic Small Round Cell Tumor
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Desmoplastic Small Round Cell Tumor Overview

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Learn About Desmoplastic Small Round Cell Tumor

What is the definition of Desmoplastic Small Round Cell Tumor?
Desmoplastic small round cell tumor (DSRCT) is a rare type of soft tissue cancer (sarcoma) that usually begins in the abdomen. It primarily affects children and young adults and is more common in males. It is formed by small, round cancer cells surrounded by scar-like tissue and is often found in the tissue (peritoneum) that lines the inside of the abdomen and pelvis. The tumor cells have a characteristic genetic change involving a translocation between chromosomes 11 and 22, which is important in differentiating from other similar tumors. The genetic change involved in DSRCT is acquired throughout a person's lifetime and is not inherited. Symptoms may include abdominal pain and a feeling of fullness, abdominal mass, and symptoms of gastrointestinal obstruction, such as constipation.
What are the alternative names for Desmoplastic Small Round Cell Tumor?
  • Desmoplastic small round cell tumor
  • DSRCT
  • Desmoplastic small round-cell tumor
Who are the top Desmoplastic Small Round Cell Tumor Local Doctors?
Peter Anderson
Elite in Desmoplastic Small Round Cell Tumor
Dr. Peter Anderson
Pediatrics
Elite in Desmoplastic Small Round Cell Tumor
Dr. Peter Anderson
Pediatrics

Cleveland Clinic Children's Outpatient Center

8950 Euclid Avenue, 
Cleveland, OH 
216-444-8950
Experience:
51+ years
Languages Spoken:
English
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Peter Anderson is a Pediatrics provider in Cleveland, Ohio. Dr. Anderson has been practicing medicine for over 51 years and is rated as an Elite provider by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. His top areas of expertise are Osteosarcoma, Ewing Sarcoma, Desmoplastic Small Round Cell Tumor, and Adult Soft Tissue Sarcoma.

Andrea L. Ferrari
Elite in Desmoplastic Small Round Cell Tumor
Andrea L. Ferrari
Elite in Desmoplastic Small Round Cell Tumor
Andrea L. Ferrari
Milan, IT 

Andrea Ferrari practices in Milan, Italy. Ms. Ferrari is rated as an Elite expert by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. Her top areas of expertise are Rhabdomyosarcoma, Adult Soft Tissue Sarcoma, Synovial Sarcoma, Thyroidectomy, and Pancreatectomy.

 
 
 
 
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Elite in Desmoplastic Small Round Cell Tumor
Dr. Vivek Subbiah
Oncology
Elite in Desmoplastic Small Round Cell Tumor
Dr. Vivek Subbiah
Oncology

Office

335 24th Ave N Ste 200, 
Nashville, TN 
615-398-9890
Languages Spoken:
English
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Offers Telehealth

Vivek Subbiah is an Oncologist in Nashville, Tennessee. Dr. Subbiah is rated as an Elite provider by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. His top areas of expertise are Adult Soft Tissue Sarcoma, Desmoplastic Small Round Cell Tumor, Ewing Sarcoma, and Osteosarcoma.

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What are the latest Desmoplastic Small Round Cell Tumor Clinical Trials?
Multimodal Immune Characterization of RAre Soft Tissue Sarcoma - MIRAS Project From SARRA (SARcome RAre) Project of the French Sarcoma Group
Multimodal Immune Characterization of RAre Soft Tissue Sarcoma - MIRAS Project From SARRA (SARcome RAre) Project of the French Sarcoma Group
Enrollment Status: Recruiting
Publish Date: February 10, 2026
Intervention Type: Other
Study Phase: Not Applicable

Summary: This trial is a translational, open-label, multi-sites, prospective and retrospective cohort study of 500 patients aimed at clinical and biological characterization of sarcoma of rare subtype. 400 patients will be included in this prospective cohort study; they will be identified in the investigating centers in the context of either routine care or a clinical study protocol. Retrospective cases of...

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Registry for Patients With Desmoplastic Small Round Cell Tumor
Registry for Patients With Desmoplastic Small Round Cell Tumor
Enrollment Status: Recruiting
Publish Date: January 12, 2026

Summary: This study is a patient registry of people with Desmoplastic Small Round Cell Tumor (DSRCT). A patient registry is a collection of health information about a group of people, and it is usually focused on a specific diagnosis or disease. The purpose of this registry is to create a database- a collection of information-or better understanding DSRCT. Researchers will use the information from this dat...

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Who are the sources who wrote this article ?

Published Date: May 02, 2022
Published By: Genetic and Rare Diseases Informnation Center