Mondini Dysplasia Latest Advances

Find the Latest Research About Mondini Dysplasia

Last Updated: 09/26/2026

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Found 266 publications

Hearing outcomes of cochlear implantation in IP-II (Mondini dysplasia) - A systematic review.

Hearing outcomes of cochlear implantation in IP-II (Mondini dysplasia) - A systematic review.

Journal: Cochlear implants international
Published: March 04, 2026

Failed cochlear implant followed by auditory brainstem implant in a patient with Mondini malformation and uncontrolled otomastoiditis: a case report.

Failed cochlear implant followed by auditory brainstem implant in a patient with Mondini malformation and uncontrolled otomastoiditis: a case report.

Journal: Journal of medical case reports
Published: December 05, 2025

Perilymphatic Fistula and Vestibular Dysfunction Requiring Cochlear Implant Programming Intervention: A Case Study.

Perilymphatic Fistula and Vestibular Dysfunction Requiring Cochlear Implant Programming Intervention: A Case Study.

Journal: Ear, nose, & throat journal
Published: July 25, 2025

Breaking the Silence: A Case for Early Intervention in Profound Adolescent Hearing Loss.

Breaking the Silence: A Case for Early Intervention in Profound Adolescent Hearing Loss.

Journal: Cureus
Published: June 08, 2025

CSF gushers in cochlear implantation: surgical planning and management.

CSF gushers in cochlear implantation: surgical planning and management.

Journal: BMC surgery
Published: May 09, 2025

The landscape of gene mutations in a cohort of 3353 Han Chinese children with nonsyndromic hearing loss.

The landscape of gene mutations in a cohort of 3353 Han Chinese children with nonsyndromic hearing loss.

Journal: EBioMedicine
Published: March 21, 2025

Using T7 endonuclease I to detect SLC26A4 mutations in children with large vestibular aqueduct syndrome, with or without Mondini malformation and assess cochlear implant outcomes.

Using T7 endonuclease I to detect SLC26A4 mutations in children with large vestibular aqueduct syndrome, with or without Mondini malformation and assess cochlear implant outcomes.

Journal: European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
Published: January 03, 2025

Patients with Mondini deformty: is standard electrode necessary?

Patients with Mondini deformty: is standard electrode necessary?

Journal: European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
Published: July 12, 2024

Clinical Phenotypic Characterization of the SLC26A4 Mutation in Pendred Syndrome/Nonsyndromic Enlarged Vestibular Aqueduct.

Clinical Phenotypic Characterization of the SLC26A4 Mutation in Pendred Syndrome/Nonsyndromic Enlarged Vestibular Aqueduct.

Journal: The Laryngoscope
Published: March 24, 2024

The role of SLC26A4 in bony labyrinth development and otoconial mineralization in mouse models.

The role of SLC26A4 in bony labyrinth development and otoconial mineralization in mouse models.

Journal: Frontiers in molecular neuroscience
Published: February 10, 2024

Enlarged vestibular aqueduct as a cause of postneonatal deafness.

Enlarged vestibular aqueduct as a cause of postneonatal deafness.

Journal: Acta otorrinolaringologica espanola
Published: August 07, 2023

Analysis of 59 cases of large vestibular aqueduct syndrome SLC26A4gene mutation frequency and new mutation sites

Analysis of 59 cases of large vestibular aqueduct syndrome SLC26A4gene mutation frequency and new mutation sites

Journal: Lin chuang er bi yan hou tou jing wai ke za zhi = Journal of clinical otorhinolaryngology head and neck surgery
Published: June 19, 2023
Showing 1-12 of 266

Last Updated: 09/26/2026