Learn About Nonsyndromic Hearing Loss
Nonsyndromic hearing loss is a partial or total loss of hearing that is not associated with other signs and symptoms. In contrast, syndromic hearing loss occurs with signs and symptoms affecting other parts of the body.
The causes of nonsyndromic hearing loss are complex. Researchers have identified more than 90 genes that, when altered, are associated with nonsyndromic hearing loss. Many of these genes are involved in the development and function of the inner ear. Mutations in these genes contribute to hearing loss by interfering with critical steps in processing sound. Different mutations in the same gene can be associated with different types of hearing loss, and some genes are associated with both syndromic and nonsyndromic forms. In many affected families, the factors contributing to hearing loss have not been identified.
Between 2 and 3 per 1,000 children in the United States are born with detectable hearing loss in one or both ears. The prevalence of hearing loss increases with age; the condition affects 1 in 8 people in the United States age 12 and older, or about 30 million people. By age 85, more than half of all people experience hearing loss.
As discussed above, nonsyndromic hearing loss has different patterns of inheritance. Between 75 and 80 percent of cases are inherited in an autosomal recessive pattern, which means both copies of the gene in each cell have mutations. Usually, each parent of an individual with autosomal recessive hearing loss carries one copy of the mutated gene but does not have hearing loss.
Duke Ambulatory Surgery Center
David Kaylie is an Otolaryngologist in Durham, North Carolina. Dr. Kaylie is rated as an Advanced provider by MediFind in the treatment of Nonsyndromic Hearing Loss. His top areas of expertise are Acoustic Neuroma, Schwannoma, Hearing Loss, Mastoidectomy, and Myringotomy. Dr. Kaylie is currently accepting new patients.
Proliance Surgeons
Peter F. Maurice, MD, is a highly specialized otolaryngologist, and fellowship-trained in plastic surgery. He is double board-certified by the American Board of Facial Plastic and Reconstructive Surgery and the American Board of Otolaryngology.Dr. Maurice received his medical degree from Georgetown University, in Washington, DC, where he was elected to membership in the Alpha Omega Alpha Honor Medical Society. He completed his residency in otolaryngology–head and neck surgery at Georgetown University Hospital.Dr. Maurice then was selected for a fellowship in facial plastic and reconstructive surgery. This full-year training program gave him a unique opportunity to study with one of the AAFPRS's master surgeons in Albuquerque, New Mexico.At South Seattle Otolaryngology, patients benefit from a team of on-site audiologists and allergy specialists, in addition to a team of otolaryngologists with over 50 years of combined experience. Dr. Maurice is rated as an Advanced provider by MediFind in the treatment of Nonsyndromic Hearing Loss. His top areas of expertise are Chronic Rhinosinusitis with Nasal Polyps (CRSwNP), Low Nasal Bridge, Nasal Septal Hematoma, and Sinusitis.
Proliance Surgeons
David Santos, MD, is board certified by both the American Board of Otolaryngology–Head and Neck Surgery and the American Board of Facial Plastic and Reconstructive Surgery.He prides himself in keeping up to date with cutting edge treatments and applying state-of-the-art techniques and technologies. He is committed to excellence in facelift surgical technique, rejuvenation, and artistry, as well as creating an environment where the best medical care and facial rejuvenation possible is achieved for each individual. Dr. Santos is rated as an Advanced provider by MediFind in the treatment of Nonsyndromic Hearing Loss. His top areas of expertise are Swimmer's Ear, Labyrinthitis, Chronic Rhinosinusitis with Nasal Polyps (CRSwNP), and Infant Hearing Loss.
Published Date: February 01, 2016
Published By: National Institutes of Health