Spinocerebellar Ataxia Type 1 Latest Advances

Find the Latest Research About Spinocerebellar Ataxia Type 1

Last Updated: 06/30/2026

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Found 284 publications

Beyond neuronal degeneration: oligodendroglial dysfunction as a driver of spinocerebellar ataxia type 1 pathogenesis.

Beyond neuronal degeneration: oligodendroglial dysfunction as a driver of spinocerebellar ataxia type 1 pathogenesis.

Journal: The Journal of clinical investigation
Published: June 15, 2026

Oligodendrocyte dysfunction contributes to motor deficits and Purkinje cell axonopathy in spinocerebellar ataxia type 1.

Oligodendrocyte dysfunction contributes to motor deficits and Purkinje cell axonopathy in spinocerebellar ataxia type 1.

Journal: The Journal of clinical investigation
Published: May 11, 2026

Neural basis for mutant ATAXIN-1 induced respiratory dysfunction in mouse models of spinocerebellar ataxia type 1.

Neural basis for mutant ATAXIN-1 induced respiratory dysfunction in mouse models of spinocerebellar ataxia type 1.

Journal: Neurobiology of disease
Published: February 04, 2026

Long term administration of selective NMDA GluN2B receptor blocker Ro25-6981 attenuates neurodegeneration in mouse model of spinocerebellar ataxia type 1 (SCA1).

Long term administration of selective NMDA GluN2B receptor blocker Ro25-6981 attenuates neurodegeneration in mouse model of spinocerebellar ataxia type 1 (SCA1).

Journal: Cell death discovery
Published: January 30, 2026

Cardiovascular Exercise Drives Neuroprotection in a Mouse Model of Spinocerebellar Ataxia 1 Via Rescue of Aberrant Splicing.

Cardiovascular Exercise Drives Neuroprotection in a Mouse Model of Spinocerebellar Ataxia 1 Via Rescue of Aberrant Splicing.

Journal: Annals of neurology
Published: January 28, 2026

Striatal pathology in Spinocerebellar Ataxia Type 1 mice: A comparative study with Huntington's disease.

Striatal pathology in Spinocerebellar Ataxia Type 1 mice: A comparative study with Huntington's disease.

Journal: bioRxiv : the preprint server for biology
Published: December 19, 2025

Generation of an isogenic human induced pluripotent stem cell line for spinocerebellar ataxia type 1.

Generation of an isogenic human induced pluripotent stem cell line for spinocerebellar ataxia type 1.

Journal: Stem cell research
Published: December 12, 2025

Early and Progressive Spinal Cord Atrophy in Spinocerebellar Ataxia Type 1.

Early and Progressive Spinal Cord Atrophy in Spinocerebellar Ataxia Type 1.

Journal: Movement disorders : official journal of the Movement Disorder Society
Published: December 09, 2025

Seven-year Follow-up of Cerebellar Type 1 Metabotropic Glutamate Receptor Availability in a Family With Spinocerebellar Ataxia Type 19/21.

Seven-year Follow-up of Cerebellar Type 1 Metabotropic Glutamate Receptor Availability in a Family With Spinocerebellar Ataxia Type 19/21.

Journal: Clinical nuclear medicine
Published: November 05, 2025

Retinal morphology in spinocerebellar ataxia type 1 (SCA1) mice: A stereological analysis across different age groups.

Retinal morphology in spinocerebellar ataxia type 1 (SCA1) mice: A stereological analysis across different age groups.

Journal: Experimental eye research
Published: November 04, 2025

Translational Relevance of SCA1 Models for the Development of Therapies for Spinocerebellar Ataxia Type 1.

Translational Relevance of SCA1 Models for the Development of Therapies for Spinocerebellar Ataxia Type 1.

Journal: Biomedicines
Published: October 23, 2025

Comparative Analysis of Two Autophagy-Enhancing Small Molecules (AUTEN-67 and -99) in a Drosophila Model of Spinocerebellar Ataxia Type 1.

Comparative Analysis of Two Autophagy-Enhancing Small Molecules (AUTEN-67 and -99) in a Drosophila Model of Spinocerebellar Ataxia Type 1.

Journal: International journal of molecular sciences
Published: September 23, 2025
Showing 1-12 of 284

Last Updated: 06/30/2026