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Familial Hypofibrinogenemia Latest Advances
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Last Updated: 01/20/2023
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Found 9 publications
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Efficacy and safety of fibrinogen concentrate for perioperative prophylaxis of bleeding in adult, adolescent, and pediatric patients with congenital fibrinogen deficiency: FORMA-02 and FORMA-04 clinical trials.
Condition:
Congenital Fibrinogen Deficiency (CFD)
Journal:
Transfusion
Treatment Used:
Fibrinogen Concentrate
Number of Patients:
12
Published:
August 06, 2022
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Congenital Fibrinogen Deficiency Caused by Novel FGG Gene Mutation.
Journal:
Zhongguo shi yan xue ye xue za zhi
Published:
April 04, 2021
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Rare severe hypofibrinogenemia induced by tissue plasminogen activator in stroke patients: Case report.
Condition:
Recombinant Tissue Plasminogen Activator-Related Symptomatic Intracranial Hemorrhage
Journal:
Medicine
Treatment Used:
Fibrinogen Replacement Therapy and Platelet Transfusion
Number of Patients:
2
Published:
March 03, 2021
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Paradoxical pulmonary hemorrhage associated with hemocoagulase batroxobin in a patient with hemoptysis: A CARE-compliant case report.
Condition:
Paradoxical Pulmonary Hemorrhage associated with Hemocoagulase Batroxobin with Hemoptysis
Journal:
Medicine
Treatment Used:
Hemocoagulase Discontinuation and Fibrinogen-Containing Plasma Administration
Number of Patients:
1
Published:
February 03, 2021
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A case of inherited afibrinogenemia caused by an IVS7-12A>G splice mutation of FGG gene.
Journal:
Zhonghua yi xue yi chuan xue za zhi = Zhonghua yixue yichuanxue zazhi = Chinese journal of medical genetics
Published:
December 11, 2020
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Bleeding characteristics and management of minor surgeries in rare bleeding disorders: report from a Turkish Pediatric Hematology Center.
Condition:
Minor Surgeries in Rare Bleeding Disorders (RBDs)
Journal:
The Turkish journal of pediatrics
Treatment Used:
Preoperative Replacement Therapies plus 5-7 Days of Antifibrinolytics
Number of Patients:
26
Published:
August 12, 2020
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Pharmacology, Efficacy and Safety of a Triple-Secured Fibrinogen Concentrate in Children Less than or Equal to 12 Years with Afibrinogenaemia.
Condition:
Children Less than or Equal to 12 Years with Afibrinogenaemia
Journal:
Thrombosis and haemostasis
Treatment Used:
Triple-Secured Fibrinogen Concentrate (FC)
Number of Patients:
16
Published:
May 12, 2020
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Fibrinogen concentrate for treatment of bleeding and surgical prophylaxis in congenital fibrinogen deficiency patients.
Condition:
Congenital afibrinogenemia
Journal:
Journal of thrombosis and haemostasis : JTH
Treatment Used:
Fibrinogen concentrate
Number of Patients:
25
Published:
December 31, 2019
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Clinical pharmacology, efficacy and safety study of a triple-secured fibrinogen concentrate in adults and adolescent patients with congenital fibrinogen deficiency.
Condition:
Congenital Fibrinogen Deficiency
Journal:
Journal of thrombosis and haemostasis : JTH
Treatment Used:
Fibrinogen Concentrate
Number of Patients:
16
Published:
January 21, 2019
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Showing 1-9 of 9
Last Updated: 01/20/2023