A Phase 3, Double-Blind, Randomized, Placebo-Controlled, Multicenter Study Evaluating the Efficacy and Safety of Mitapivat in Subjects With Transfusion-Dependent Alpha- or Beta-Thalassemia (ENERGIZE-T)

Who is this study for? Patients with transfusion-dependent alpha- or beta-thalassemia
What treatments are being studied? Mitapivat
Status: Active_not_recruiting
Location: See all (75) locations...
Intervention Type: Drug
Study Type: Interventional
Study Phase: Phase 3
SUMMARY

The primary objective of this study was to compare the effect of mitapivat versus placebo on transfusion burden in participants with α- or β-transfusion-dependent thalassemia.

Eligibility
Participation Requirements
Sex: All
Minimum Age: 18
Healthy Volunteers: f
View:

• Greater than or equal to (≥)18 years of age at the time of providing informed consent;

• Documented diagnosis of thalassemia (β-thalassemia with or without α-globin gene mutations, hemoglobin E (HbE)/β-thalassemia, or α-thalassemia/hemoglobin H (HbH) disease) based on deoxyribonucleic acid (DNA) analysis;

• Considered transfusion-dependent, defined as 6 to 20 red blood cells (RBC) units transfused and ≤6-week transfusion-free period during the 24-week period before randomization;

• If taking hydroxyurea, the hydroxyurea dose must be stable for ≥16 weeks before randomization;

• Women of childbearing potential (WOCBP) must be abstinent of sexual activities that may induce pregnancy as part of their usual lifestyle or agree to use two forms of contraception, one of which must be considered highly effective, from the time of providing informed consent, throughout the study, and for 28 days after the last dose of study drug. The second form of contraception can be an acceptable barrier method;

• Written informed consent before any study-related procedures are conducted and willing to comply with all study procedures for the duration of the study.

Locations
United States
Arizona
Phoenix Children's Hospital
Phoenix
California
San Diego Hospital, UC San Diego Health
La Jolla
Children's Hospital Oakland
Oakland
Stanford Medicine
Palo Alto
Massachusetts
Boston Children's Hospital
Boston
Michigan
Children's Hospital of Michigan
Detroit
North Carolina
Duke University Medical Center
Durham
New York
Weill Cornell Medical Center
New York
Pennsylvania
Penn Medicine - University of Pennsylvania Health System
Philadelphia
Washington
Seattle Cancer Care Alliance, University of Washington
Seattle
Other Locations
Brazil
Hospital Das Clínicas da Faculdade de Medicina de Ribeirão Preto - USP
Ribeirão Preto
GSH Banco de Sangue de São Paulo
São Paulo
Bulgaria
MHAT Dr. Nikola Vasiliev AD
Kyustendil
UMHAT Dr. Georgi Stranski Pleven
Pleven
UMHAT Sveti Georgi EAD
Plovdiv
SHATHD Sofia
Sofia
UMHAT Prof. Dr. Stoyan Kirkovich
Stara Zagora
Canada
Foothills Medical Centre
Calgary
Toronto General Hospital, University Health Network
Toronto
Denmark
Rigshospitalet
Hovedstaden
France
CHU Hôpital Henri Mondor
Créteil
Hôpital Edouard Herriot, CHU de Lyon
Lyon
CHU Hôpital de la Timone
Marseille
Hôpital Necker Enfants Malades
Paris
Germany
Charité - UB - CVK - Medizinische Klinik
Berlin
Universitätsklinikum Essen
Essen
Universitätsklinikum Leipzig
Leipzig
Greece
University General Hospital of Patras
Achaia
Children's Hospital Agia Sophia, National and Kapodistrian University of Athens Medical School
Athens
Laiko General Hospital
Athens
University Hospital of Ioannina
Ioannina
Ippokrateio General Hospital
Thessaloniki
Italy
Ospedale A. Perrino - Brindisi
Brindisi
Ospedale Pediatrico Microcitemico
Cagliari
Ospedale Sant'Anna
Ferrara
Ente Ospedaliero Ospedali Galliera
Genova
Fondazione IRCCS Cà Granda Ospedale Maggiore Policlinico
Milan
A.O.U Di Modena
Modena
AOU L. Vanvitelli Universita degli Studi della Campania Luigi Vanvitelli
Napoli
A.O.U. San Luigi Gonzaga
Orbassano
Lebanon
Chronic Care Center
Beirut
Malaysia
Hospital Sultanah Bahiyah
Alor Star
Hospital Sultanah Aminah Johor Bahru
Johor Bahru
Hospital Queen Elizabeth, Kota Kinabalu
Kota Kinabalu
Hospital Tunku Azizah
Kuala Lumpur
Hospital Tengku Ampuan Afzan
Kuantan
Hospital Umum Sarawak
Kuching
Hospital Ampang
Pandan Indah
Hospital Pulau Pinang
Pulau Pinang
Netherlands
Amsterdam Universitair Medisch Centrum, Locatie AMC
Amsterdam
Universitair Medisch Centrum Utrecht
Utrecht
Erasmus MC
Westzeedijk 353
Saudi Arabia
King Abdullah International Medical Research Center
Riyadh
King Khalid University Hospital
Riyadh
Spain
Hospital Universitario Vall d'Hebron
Barcelona
Hospital Universitario La Paz
Madrid
Hospital Universitario Virgen Arrixaca
Murcia
Hospital Universitario Virgen del Rocío
Seville
Taiwan
National Taiwan University Hospital
Taipei
Thailand
Faculty of Medicine Siriraj Hospital
Bangkok
Phramongkutklao Hospital
Bangkok
Ramathibodi Hospital
Bangkok
Maharaj Nakorn Chiang Mai Hospital
Chiang Mai
Srinagarind Hospital, Khon Kaen University
Khon Kaen
Naresuan University Hospital
Mueang Phitsanulok
King Chulalongkorn Memorial Hospital
Pathum Wan
Turkey
Acibadem Adana Hospital
Adana
Akdeniz University Faculty of Medicine
Antalya
Çukurova University
Balcalı
Ege University Faculty of Medicine
Bornova
Istanbul University Faculty of Medicine
Fatih
Hacettepe University
Mersin
United Arab Emirates
Burjeel Medical City
Abu Dhabi
United Kingdom
Imperial College Healthcare NHS Trust - Hammersmith Hospital
London
University College London
London
Time Frame
Start Date: 2021-11-30
Completion Date: 2029-06
Participants
Target number of participants: 258
Treatments
Experimental: Mitapivat
Participants randomized to receive mitapivat 100 milligrams (mg), orally, twice daily (BID) for 48 weeks in the double-blind (DB) period and for up to 5 years in the open label extension (OLE) period.
Placebo_comparator: Placebo
Participants randomized to receive placebo matching mitapivat, orally, BID for 48 weeks in the DB period followed by mitapivat 100 mg, orally, BID for up to 5 years in the OLE period.
Sponsors
Leads: Agios Pharmaceuticals, Inc.

This content was sourced from clinicaltrials.gov